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报道两例Hb M Iwate[α87(F8)His→Tyr),并对其结构与功能的关系进行了较全面的研究,发现此异常Hb的特异性吸收光谱和氧平衡特征均与文献报道相符。文中对 Hb M病导致紫绀的机理提出了新的看法。
Two cases of Hb M Iwate [α87 (F8) His → Tyr) were reported and the relationship between their structure and function was comprehensively studied. The results showed that the specific absorption spectra and oxygen balance characteristics of Hb were consistent with those reported in the literature. The article put forward a new view on the mechanism of cyanosis caused by Hb M disease.