1病历介绍患者,女,67岁。因进行性皮肤、巩膜黄染伴皮肤瘙痒半月,近日出现酱油色尿液及大便白陶土色就诊。9年前,因腹部不适经B超检查,发现先天性胆总管囊肿,未治。本次就诊实验室检查:总胆红素216.70μmol/L,直接胆红素181.90μmool/L,间接胆红素34.79μmol/L,总胆汁酸217.8μ Patient, female, 67 years old. Due to progressive skin, scleral yellow dye with itchy skin half months, the recent emergence of soy sauce color urine and stool white clay color treatment. 9 years ago, due to abdominal discomfort by B-ultrasound and found that congenital choledochal cyst, not cured. The visit laboratory examination: total bilirubin 216.70μmol / L, direct bilirubin 181.90μmool / L, indirect bilirubin 34.79μmol / L, total bile acid 217.8μ