论文部分内容阅读
对患有非进行或缓慢进展性神经肌肉疾病的年轻患者,提供夜间辅助通气大有裨益,这已有数例报道。本文报道8例患有夜间通气不足症患者,重要的是临床特征及其中7例治疗成功的经验。病例及方法8例患者年龄在4～24岁,均有症状,呈进行性清晨头痛、嗜睡和呕吐,急性感染可有呼吸衰竭和肺心病,7例能行走。以睡眠不安为其特征,有时症状长达几年,5例有脊柱侧弯35°～60°,2例患Emery Dreifuss 肌营养不良,颈部和背部活动受限。仰卧时观察胸壁运动,所有患者均无腹肌的矛盾运动,立位时有不正常的呼吸肌运动。
There have been several reports of nocturnal assisted ventilation in young patients with non-progressing or slowly progressive neuromuscular diseases. This article reports on 8 patients with nocturnal hypoventilation who are clinically important and of whom 7 have successful treatment. Cases and methods 8 patients aged 4 to 24 years old, have symptoms, progressive early morning headache, lethargy and vomiting, acute respiratory failure may have respiratory failure and pulmonary heart disease, 7 cases were able to walk. Restlessness is characterized by sleepiness, symptoms sometimes up to several years, 5 cases of scoliosis 35 ° ~ 60 °, 2 cases of Emery Dreifuss muscular dystrophy, limited neck and back movement. Abdominal observation of chest wall movement, all patients have no contractility abdominal muscles, standing position when there is abnormal respiratory muscle movement.