患者,女,17岁。阵发性咳嗽伴进行性呼吸困难1年,劳累或气候变化时呼吸困难加重,1999年5月28日急诊入院。入院当天因喉梗阻吸气性呼吸困难度,濒于窒息。立即行气管切开术,气管内涌出大量粘脓痰。血压、脉搏、心电图均正常。身体瘦弱,体重38.5kg。5d后纤维喉镜检查见,声门下1.5～ Patient, female, 17 years old. Paroxysmal cough with progressive dyspnea for 1 year, aggravated breathing during exertion or climate change, emergency hospital admission on May 28, 1999. On the day of admission, inhaled dyspnea due to laryngeal obstruction was associated with suffocation. Tracheotomy was performed immediately and a large amount of mucopus spewed in the trachea. Blood pressure, pulse, and electrocardiogram were normal. The body is thin and weighs 38.5kg. After 5 days of fiberoptic laryngoscopy, see 1.5 to below the glottis