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对34例因血液系统疾病而脾切除患儿进行远期随访。随访34例中死亡15例,14例死因为原发病加感染占93.3%。在术后2年内死亡有10例,存活病儿中有14例进行门诊随访;随访时间与切脾相距1~17年。病程中出现反复呼吸道感染、肺炎、化脑、伤寒6例占42.8%,进行体液及细胞免疫检查:IgM、淋巴细胞转化及花环形成、CD4/CD8、CH50、C3有90%患儿均有不同程度的降低。NAP阳性率与积分在正常范围。
Long-term follow-up was performed on 34 children with splenectomy due to blood diseases. Follow-up 34 cases died in 15 cases, 14 cases of death due to primary disease and infection accounted for 93.3%. There were 10 deaths within 2 years after operation and 14 out of 55 surviving children were followed up for an outpatient visit. The follow-up time was 1 to 17 years after the splenectomy. There were 6 cases (42.8%) with respiratory tract infection, pneumonia, brain injury and typhoid fever in the course of the disease. Humoral and cellular immunity tests were performed: IgM, lymphocyte transformation and rosette formation. 90% of CD4 / CD8, CH50 and C3 children There are different degrees of reduction. NAP positive rate and integral in the normal range.