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患婴,女,出生1天,因产后全身发紫半小时,产科拟诊“新生儿窒息,新生儿发育畸形”而转入儿科。体查:体温不升,呼吸稍促,反应稍差,全身皮肤轻度发绀;双眼距宽,鼻大而扁平;双肺呼吸音粗,未闻及干湿性罗音,心界不大,心率124次/分,律齐,心尖区闻及Ⅲ°舒张期杂音。腹及四肢未见明显异常,肌张力稍低,生理反射存在。胸片示:①心肺未见异常;②石骨症;③蝴蝶椎。头颅CT未见异常。临床疑有先天性心脏病而申请彩色多普勒超声心动图(彩超)检查。彩超所见:左房、左室及右房大小正常,右室扩
Baby, female, born 1 day, due to postpartum body purple half an hour, obstetric consultation “neonatal asphyxia, neonatal malformation ” and transferred to pediatrics. Physical examination: body temperature does not rise, breathing a little faster, the reaction is slightly worse, mild cyanosis of the whole body skin; eyes wide and wide nose big and flat; lung breath sounds rough, unheard and wet and dry rales, Heart rate 124 beats / min, law Qi, apex area smell and Ⅲ ° diastolic murmur. No significant abdominal and limb abnormalities, muscle tone slightly lower, there is physiological reflex. Chest X-ray showed: ① heart and lung no abnormalities; ② bone disease; ③ butterfly vertebra. Head CT no abnormalities. Clinical suspected congenital heart disease and apply for color Doppler echocardiography (color Doppler ultrasound) examination. Ultrasonography seen: left atrium, left ventricular and right atrial normal size, right ventricular expansion