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目的 探讨原发性结外恶性淋巴瘤的临床特点、病理类型、易误诊的原因,总结其诊断和治疗的经验。方法 回顾性分析广东省佛山市第一医院1996-01 ~2000 -12经病理确诊的原发于结外的恶性淋巴瘤共50例。结果 发生于胃肠道者25例,咽淋巴环9例,中枢神经系统4例,脾淋巴瘤5例,甲状腺4例,乳腺1例,骨2例。均为非霍奇金淋巴瘤(NHL)。免疫组化分析以B细胞型为主。临床表现复杂,多易误诊。术后进行化疗和放疗的效果好。结论 原发性结外恶性淋巴瘤临床表现因病变部位不同而异。对疑诊病例应尽早手术,术后放疗和化疗可以取得较好的疗效。
Objective To investigate the clinical features, pathological types and causes of misdiagnosis of primary malignant lymphoma and summarize the experience of diagnosis and treatment. Methods A retrospective analysis of the first hospital in Foshan City, Guangdong Province, 1996-01 ~ 2000 -12 pathologically confirmed primary malignant lymphoma in 50 cases. Results 25 cases occurred in the gastrointestinal tract, 9 cases of pharyngeal lymph nodes, central nervous system in 4 cases, 5 cases of splenic lymphoma, thyroid in 4 cases, 1 case of breast, bone in 2 cases. All non-Hodgkin’s lymphoma (NHL). Immunohistochemical analysis of B cell type based. Clinical manifestations of complex, more easily misdiagnosed. Postoperative chemotherapy and radiotherapy good effect. Conclusion The clinical manifestations of primary extranodal malignant lymphoma vary with the location of the lesion. As soon as possible on suspected cases of surgery, postoperative radiotherapy and chemotherapy can achieve better results.