由于先天性巨结肠是肠道肌间及黏膜下神经元缺乏及发育异常,肠壁的肌肉不收缩,不能把粪便挤出肠外,造成排便困难,因此治疗的首要目的是使患儿能够排便。为了达到这个目的,医生们采取了两种主要治疗手段:姑息性治疗和根治性治疗。形成了尽量少分离直肠前壁、切开肛门内括约肌的范围要适当、拖出肠管要有正常神经节细胞及术前要充分考虑术后可能出现的便秘及失禁问题等 Hirschsprung’s disease is due to lack of intestinal and submucosal neurons and dysplasia, muscle contraction of the intestinal wall, can not be excreted outside the intestine, resulting in defecation difficulties, so the primary purpose of treatment is to enable children to defecation . To achieve this goal, doctors have adopted two main types of treatment: palliative and radical treatment. Formed as little as possible to separate the anterior rectal wall, cut the scope of the anal sphincter to be appropriate, out of the bowel should have normal ganglion cells and preoperative to give full consideration to possible postoperative constipation and incontinence problems