目的　为降低非松果体区生殖细胞瘤的误诊率。方法　对近 5 a来误诊的非松果体区生殖细胞瘤 12例的临床资料加以总结。结果　 5例误诊为颅咽管瘤 ,3例误诊为垂体瘤 ,3例误诊为胶质瘤 ,1例误诊为转移瘤。结论　凡年龄在 13岁左右的患儿 ,如出现尿崩症或一侧肢体乏力 ,应考虑本症可能 ;如进一步发现松果体区病灶 ,即可确诊 ;必要时可行试验性放射治疗 The purpose is to reduce the misdiagnosis rate of non-pineal body germ cell tumor. Methods The clinical data of 12 patients with misdiagnosed non-pineal germ cell tumors in recent 5 years were summarized. Results 5 cases were misdiagnosed as craniopharyngiomas, 3 cases misdiagnosed as pituitary tumors, 3 cases misdiagnosed as gliomas and 1 case misdiagnosed as metastases. Conclusion All patients aged 13 years old should have their disease diagnosed if they have diabetes insipidus or one side of their limbs. If the lesions of the pineal region are further found, they can be diagnosed. If necessary, experimental radiotherapy