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组织细胞增生症X是以组织细胞为主的网状内皮细胞增殖而形成的肉穿肿,包括嗜酸细胞肉芽肿、韩-薛-柯综合征及勒-雪综合征等3型。前2型易出现骨病变,颅骨受累最多见,其次为股骨、肋骨、骨盆、肱骨及脊椎。脊椎病变多在胸腰椎,颈椎受累非常罕见。病例7岁2个月男患,入院前1个月左颈部疼痛,局部肿胀,曾因诊断淋巴结炎用抗主素治疗而无
The histiocytosis X is a meat edema formed by proliferation of reticuloendothelial cells mainly composed of tissue cells, including 3 types of eosinophilic granuloma, Han-Schaecher syndrome, and Le-Snow syndrome. The former type 2 prone to bone lesions, the most common skull involvement, followed by the femur, ribs, pelvis, sacrum and spine. Spinal lesions are mostly in the thoracolumbar spine, and cervical involvement is very rare. The patient was 7 years old and 2 months old. He had left neck pain and local swelling 1 month before admission. He had been treated with anti-tumor agents for the diagnosis of lymphadenitis.