结节性硬化是累及全身多器官,包括皮肤、脑和内脏的错构瘤样发育异常[1] ,为少见常染色体显性遗传性皮肤神经综合征。1986年6月以来,我院共发现2 3例,均行CT检查,其中1例并发多脏器肿瘤。现着重分析脑钙化结节及并发多器官肿瘤CT表现特点,以便为今后诊断与鉴别诊断该病提供参考 Tuberous sclerosis is a hamartoma-like dysplasia involving the whole body and multiple organs, including the skin, brain and internal organs [1], a rare autosomal dominant hereditary cutaneous neurological syndrome. Since June 1986, a total of 23 cases have been found in our hospital, all underwent CT examination. One case complicated with multiple organ tumors. It is important to analyze the calcified nodules and CT features of multiple organ tumors in order to provide a reference for the future diagnosis and differential diagnosis of the disease