目的 :探讨眼眶神经纤维瘤的临床表现和治疗方法。方法 :术前应用 X线、B超、CT和 MRI作检查 ,通过不同手术方法切除肿瘤并作组织病理学检查。结果 :诊断眼眶神经纤维瘤的 13例中 ,孤立型 4例 (30 .8% )、丛状型 6例 (4 6 .2 % )、弥漫型 3例(2 3.1% )。治疗均为手术切除肿瘤并作眼睑或眼窝重建术。结论 :彻底切除肿瘤及受累眼眶内容并作缺损眼睑及眼窝重建术是治疗该病的良好方法 Objective: To investigate the clinical manifestations and treatment of orbital neurofibroma. Methods: Preoperative application of X-ray, B-ultrasound, CT and MRI for examination, by different surgical methods to remove the tumor and histopathological examination. Results: Of the 13 cases diagnosed orbital neurofibroma, 4 were isolated (30.8%), 6 were plexiform (46.2%) and 3 were diffuse (21.1%). The tumors were surgically resected and treated with eyelid or orbital reconstruction. Conclusions: Thorough resection of the tumor and affected orbital contents and loss of eyelids and orbital reconstruction are good ways to treat the disease