在肿瘤组织中含有纤毛型上皮的颅咽管瘤极为罕见, 被称作纤毛型颅咽管瘤。迄今只有12例文献报道。本文报道一例酷似病例。 1 病史资料:12岁男孩,因两次急起头痛、恶心、嗜睡而在外院诊断为鞍上蛛网膜囊肿、急性梗阻性脑积水, 并于一年内两次接受急诊内窥镜下囊肿壁部分切除并第三脑室造瘘术。第二次术后半年内门诊随访,患儿无明显临 Craniopharyngiomas with ciliated epithelium in the tumor tissue are extremely rare and are called ciliated craniopharyngiomas. So far only 12 cases reported in the literature. This article reports a case resembles a case. A history of data: 12-year-old boy, twice as acute headache, nausea, drowsiness and in the outer hospital diagnosed as suprasellar arachnoid cyst, acute obstructive hydrocephalus, and within one year twice under emergency endoscopic cyst wall Partially resected and third ventricle ostomy. The second postoperative ambulatory follow-up within six months, no significant clinical children