肝豆状核变性在儿科并不罕见,若能早期诊断,将对治疗和预后均有较大的影响。但因临床类型多样,常致漏诊或误诊。现结合我院1974—1980年19例住院病儿的临床资料,报导如下。一、一般资料起病年龄4—8岁10例,9—14岁9例,平均年龄8岁零8月;就诊时年龄6—8岁6例,9—14岁13例。19例中男10例,女 Hepatolenticular degeneration is not uncommon in pediatrics, if early diagnosis, will have a greater impact on the treatment and prognosis. However, due to the diversity of clinical types, often caused by missed diagnosis or misdiagnosis. Now with our hospital from 1974-1980 19 cases of hospitalized children’s clinical data, reported as follows. First, the general information Age of onset 4-8 years in 10 cases, 9-14 years in 9 cases, the average age of 8 years and 8 months; when the age of 6-8 years old 6 cases, 9-14 years old in 13 cases. 19 cases of male 10 cases, female