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严重血友病如不积极治疗,危害很大,因为反复出血使关节、肌肉损害,神经损伤。经常的自发性出血使儿童失学、成人失业,并导致终生丧失劳动力和与社会隔离。严重的血友病人在急诊室、门诊、病房就医,浪费时间,引起债务,常成为公众的负担。随着冷沉淀物及凝血因子浓缩剂的有效应用,这种治疗对病人和社会成了未予承认的负担。当过去的十年中这点变得清楚后,现在医师、健康督导员、立法者以及国家血友病基金协作组织以新的试验方法提供了更好的医疗。这些试验包括自我治疗或家庭护
Severe hemophilia, if not actively treated, is very harmful because repeated bleeding causes joint and muscle damage and nerve damage. Frequent spontaneous bleeding causes children to lose school, adults become unemployed, and leads to a lifetime loss of labor and social isolation. Severe hemophilia patients seek medical treatment in emergency rooms, outpatient clinics, and wards, wasting time, causing debt, and often become public burdens. With the effective application of cryoprecipitates and clotting factor concentrates, this treatment has become an unacknowledged burden on patients and society. When this became clear in the past decade, physicians, health supervisors, legislators, and the National Hemophilia Fund Collaborative now provide better medical care with new test methods. These trials include self-care or home care