噬血细胞综合征(hemophagocytic syndrome,HPS)又名噬血细胞性淋巴组织细胞增生症(hemophagocytic lymphohistiocytosis,HLH),是病因及发病机制复杂、组织病理学表现为噬血活性而临床表现相类似的一组症候群。HPS多见于儿童,大多发生于血液系统肿瘤;成人患者极为罕见,发生于非血液系统肿瘤者也较为罕见[1]。本文报 Hemophagocytic syndrome (hemophagocytic syndrome, hemophagocytic lymphohistiocytosis, also known as hemophagocytic lymphohistiocytosis (HLH), is a group of patients with similar pathogenesis and pathogenesis, histopathological manifestations of hemophagocytic activity and clinical manifestations Syndrome. HPS more common in children, mostly in hematological tumors; adult patients is extremely rare, occurred in non-hematological tumors are also relatively rare [1]. This article reported