患者女,9岁。临床表现心悸、气短、口唇发绀、杵状指9年,心脏超声提示先天性心脏病。CT所示:心尖位于左侧,单心房,双侧心耳表现左心耳形态,房间隔未见(图1),心内膜垫完全未见显示,心房借两组房室瓣与两心室相连,室间隔上部延续性中断14 mm(图2),左心室无大动脉连接,右心室与主动脉相连接(图3),主 Female patient, 9 years old. Clinical manifestations palpitations, shortness of breath, cyanosis of the lips, clubbing refers to 9 years, cardiac ultrasound prompted congenital heart disease. CT showed: apex is located on the left, single atrium, bilateral atrial appendage left atrial appendage morphology, atrial septal no seen (Figure 1), no signs of endocardial cushion showed that the atrium by two atrioventricular valve and the two ventricle connected, Continuation of the interventricular septum interrupted 14 mm (Figure 2), the left ventricle without aortic connection, the right ventricle and the aorta connected (Figure 3), the main