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患女,33岁.1983年12月14日以头晕、乏力1年之主诉入院。查体:血压14.5/9.5kPa重度贫血貌,皮肤巩膜轻度黄染。心界不大,心率102次/min,律齐。腹软,肝肋下2cm,脾肋下5cm,质均中等。入院后多次抽血有自凝、自溶现象。实验室检查Hb60g/L.WBC5.4×10~9/L,PC125×10~9/L,Ret0.079。血消铁、出凝血时间均正常。尿含铁血黄素试验阴性。SGPT1584nmo/s,ZnTT19,总胆红素13.6μmol/L。胸透心肺未见异常。骨髓示增生性贫血。血中2次均未找到狼疮细胞。Coomb′s 试验盲接1∶1024(+)。间接1∶5012
Female, aged 33. December 14, 1983 to dizziness, fatigue, 1 year admitted to the main complaint. Physical examination: blood pressure 14.5 / 9.5kPa severe anemia, skin scleral mild yellow dye. Heart, heart rate 102 times / min, law Qi. Abdominal soft, liver ribs 2cm, 5cm under the spleen ribs, medium quality. Many times after admission blood self-coagulation, autolysis phenomenon. Laboratory tests Hb60g / L.WBC5.4 × 10 ~ 9 / L, PC125 × 10 ~ 9 / L, Ret0.079. Blood iron, a clotting time are normal. Urine hemosiderin test negative. SGPT1584nmo / s, ZnTT19, total bilirubin 13.6μmol / L. Thoracic heart and lung no abnormalities. Marrow showed hyperplastic anemia. Lupus cells were not found in blood for 2 times. Coomb’s Test Blind 1:1024 (+). Indirect 1:5012