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1970年Enzinger根据62例患者的自然病史、临床病理相互联系和文献复习,提出一类新的软组织恶性肿瘤,命名为上皮样肉瘤。至今又有大约80新病例报导。目前对此肉瘤的组织起源意见不一,作者从603例软组织肉瘤登记档案中收集四例诊断为上皮样肉瘤,着重组织起源的观察。患者年龄自8至21岁,部位均在四肢,分别为左足跟、右手鱼际、左腿、左肘关节部,大小从1×1到3×3 cm,治疗起初均是局部切除,2例因局部复发而截肢,发现肿瘤至手术相隔5个月至4年不等。术后随访2年到4年,患者均健存。肿瘤大体呈多结节、疤痕样或瘤块,位于皮肤、
In 1970 Enzinger proposed a new class of soft tissue malignancies, named epithelioid sarcoma, based on the natural history, clinical pathology, and literature review of 62 patients. So far there have been about 80 new cases reported. At present, there are different opinions on the origin of this sarcoma. The author collected four cases of epithelioid sarcoma from 603 soft tissue sarcoma registration files, focusing on the observation of the origin of the tissue. The patients ranged in age from 8 to 21 years old and were located on all four limbs. They were left heel, right hand intercircular, left leg, and left elbow joints. The size ranged from 1×1 to 3×3 cm. The treatment was initially performed with local resection and 2 patients. The amputation was due to local recurrence and it was found that the tumors ranged from 5 months to 4 years apart. After 2 to 4 years of follow-up, all patients survived. Tumors are mostly multinodular, scar-like, or tumorous, located on the skin,