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患儿,2岁,半年前出现阴茎逐渐肥大、增长、增粗,包皮上翻,食欲、大便正常,小便清,无发热。查体:腹膨隆,无明显压痛,未触及明显包块,肝脾触及不满意。化验:睾丸酮55.92μmol/d,尿17-羟1.73μmol24小时。B超示左上腹部实质性肿块。CT示腹块可能来自肝脏。手术见肿块来自肝左外叶,约7cm×10cm×10cm,占据大部分腹腔。切除肝左外叶和肿块,病理报告为肝母细胞瘤。术后睾丸酮0.44ng/dl。
In children, at the age of 2 years, the penis gradually became hypertrophic, increased and thickened, the foreskin turned upside down, appetite and stool were normal, urine was clear, and there was no fever. Physical examination: abdominal distension, no obvious tenderness, no obvious palpable mass, and unsatisfactory liver and spleen touch. Test: testosterone 55.92μmol/d, urine 17-hydroxyl 1.73μmol 24 hours. B ultrasound shows a solid mass in the left upper abdomen. CT may be from the liver. The operation showed that the tumor was from the left external lobe of the liver, about 7cm x 10cm x 10cm, occupying most of the abdominal cavity. Left hepatic lobes and tumors were resected and pathological reports were hepatoblastomas. Postoperative testosterone 0.44 ng/dl.