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目前对发生在肾脏的多成分结缔组织的肿瘤尚有不同的观点。大多数学者常以肿瘤组织的成分命名;有些学者对这种病是否为肿瘤表示怀疑,并认为它是发育缺陷所致的疾患,而不是真性肿瘤。多数学者认为本病是在发育不良的基础上发生的肿瘤。一般报导50~60%的肾血管平滑肌脂肪瘤可合并结节性硬性。肿瘤直径大小可从1毫米到20厘米,重量大者可达3公斤。肿瘤可单发也可多发,大部分为单侧的,双侧发病较少。本病多发生在中年女性,小儿和老年人较少见。
At present, there are still different opinions on the multi-component connective tissue tumors that occur in the kidneys. Most scholars often name the components of tumors; some scholars are skeptical about whether the disease is a tumor, and think it is a disease caused by a developmental defect, rather than a true tumor. Most scholars believe that this disease is a tumor that occurs on the basis of dysplasia. It is generally reported that 50 to 60% of renal angiomyolipoma can be combined with nodular rigidity. The diameter of the tumor can range from 1 to 20 cm, and the weight can reach 3 kg. Tumors can be single or multiple, with most of them unilateral and less frequent on both sides. The disease occurs in middle-aged women, and children and the elderly are less common.