嗅神经细胞瘤较少见,肿瘤可发生于任何年龄的患者,患者具有两个发病高峰年龄,第一个为10～20岁,第二个为50～60岁,肿瘤较多见于男性患者。显微镜下见肿瘤的形态及瘤细胞的类型较为多样,可分为四级。作者对嗅神经母细胞瘤的临床病理学特点、肿瘤分型和分级、鉴别诊断及预后等方面研究进展作一综述。 Olivary neuroblastoma is rare, the tumor can occur in patients of any age, the patient has two peak age of onset, the first 10 to 20 years old, the second for the 50 to 60 years old, the tumor is more common in male patients. Microscopic tumor morphology and tumor cells are more diverse types can be divided into four. The author reviews the clinical and pathological features of olfactory neuroblastoma, the classification and classification of tumors, differential diagnosis and prognosis.