目的　结合病理分析巨脑回畸形CT表现特点。方法　回顾性分析 7例巨脑回畸形资料。结果　巨脑回畸形CT影像特征性的表现大脑半球脑回增宽 ,脑皮层增厚 ,皮层内表面光滑 ,白质变薄。合并其他脑先天畸形 4例。结论　CT能良好显示巨脑回畸形的病理解剖学特征 Objective To analyze the CT features of giant brain deformity combined with pathology. Methods Retrospective analysis of 7 cases of giant brain deformity data. Results The characteristic features of CT images of the recurrent giant brain were as follows: widening of cerebral hemispheres, thickening of cerebral cortex, smooth inner surface of cortex and thinning of white matter. Other brain congenital malformations in 4 cases. Conclusion CT can well show the pathological anatomy of the giant brain deformity