作者报告5例发生于胫骨上端胫内侧引起骨胫内翻的局限性纤维软骨发育不良症,其中3例畸形自行矫正,2例行手术治疗。本症是1985年Bell等所命名,其特点是:(1)幼儿发病(9～28月);(2)病变位于胫骨上干骺端内侧,右侧较多;(3)胫骨呈内翻畸形;(4)X线表现为骨皮质呈“V”形缺损;(5)组织学表现为骨质缺损区由纤维软骨和腱样胶原纤维代替;(6)病变消失时间为2～4年;(7)手术治疗的并发症为胫骨外翻和神经疾患。作者认 The authors reported 5 cases of fibrillary cartilage dysplasia that occurred in the medial tibial aspect of the tibia that caused tibial varus, of which 3 were self-correcting deformities and 2 were surgically treated. The disease is named Bell et al in 1985, which is characterized by: (1) the incidence of young children (9-28 months); (2) lesions located in the medial tibia metaphyseal, the right side more; (3) Deformity; (4) X-ray showed cortical bone was “V” -shaped defect; (5) histological manifestations of bone defect area by fibrocartilage and tendon-like collagen fibers instead of; (6) lesions disappear for 2 to 4 years ; (7) complications of surgical treatment of tibial valgus and neurological disorders. The author recognizes