Spontaneous cerebrospinal fluid (CSF) rhinorrhea is rarely found, especially in patients with brain tumors.Similarly, reports of tentorial meningioma coexisting with acquired Chiari Ⅰ malformation with hydromyelia are also few. No doubt, one patient with cerebrospinal fluid rhinorrhea, tentorial meningioma and Chiari Ⅰ malformation with hydromyelia is hardly ever found. We reported one case of this rare condition.