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目的 观察肌张力障碍 (myodystonia)患者的临床表现。 方法 用回顾性方法对 2 92例肌张力障碍患者进行发病年龄与最先累及部位、是否发展到其他部位 ,及主要临床类型发病情况与性别的关系的相关性分析。结果 原发型肌张力障碍患者中较早发病者最先容易累及肢体 (5 1例 ,P <0 0 1) ;而成年起病的患者病变通常在头颈部 (14 1例 ,P <0 0 1)。痉挛性斜颈、眼睑痉挛在女性好发 ;书写痉挛和发作性肌张力障碍则男性多发。结论 肌张力障碍的临床表现呈多样化 ,各个类型的发病年龄、受累部位和男女患病率均有差异。
Objective To observe the clinical manifestations of myodystonia. Methods A retrospective analysis of 2 92 cases of dystonia in patients with age at onset and the first involving the site, whether to other parts of the development and the incidence of major clinical types and gender relationship analysis. Results The patients with early onset of dystonia were the first to be involved easily in the limbs (51 cases, P <0.01), while the patients with onset of ADHD usually had head and neck lesions (141 cases, P <0 0 1). Spasmodic torticollis, blepharospasm is good in women; writing cramps and paroxysmal dystonia are men with multiple. Conclusion The clinical manifestations of dystonia are diversified. The age of onset, the affected parts and the prevalence of men and women are different for all types of dystonia.