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多发性神经纤维瘤,又称Von Recklinghausen氏病或丛状神经纤维瘤,属神经纤维瘤(Neuro—Fibroma)之特殊类种。此病在临床上并非少见,为一遗传性神经系统(尤其是周围神经系统)发育障碍之疾,表现为周围神经多发性肿瘤样增生,可发生于交感神经、运动神经及感觉神经,常与脑膜瘤伴发,亦有时与脂肪瘤、皮脂腺瘤、毛发过度生长、成色素细胞增殖等同时存在。最常见之特征为:1.皮下特点:黄棕色皮下色素沉着,呈大小木等硬结状物,镜下见长梭形细胞排列成束。2.其他器官(颅内,视、听、三义神经脊髓核等)直接间接
Multiple neurofibroma, also known as Von Recklinghausen’s disease or plexiform neurofibroma, is a special genus of Neuro-Fibroma. The disease is not uncommon in clinical practice for a hereditary nervous system (especially the peripheral nervous system) developmental disorders disease, manifested as multiple peripheral tumor-like hyperplasia, can occur in the sympathetic, motor and sensory nerve, often with Meningioma with, sometimes also with lipoma, sebaceous adenoma, hair overgrowth, proliferation of pigmented cells exist at the same time. The most common features are: 1. Subcutaneous features: yellow-brown subcutaneous pigmentation, showed the size of wood and other hard-knot objects, microscopic spindle spindle cells arranged in bundles. 2. Other organs (intracranial, visual, hearing, Sanyi nerve spinal cord, etc.) directly