患者,男,19岁。因皮肤,眼睛反复发黄及贫血已长达9年,于1978年8月18日入院。患者自幼即面黄肌瘦,时常间断性发热,同时伴皮肤、眼睛反复发黄和贫血,时轻时重,曾接受保肝药物治疗,因无效前来住院。查体:营养状态欠佳,呈贫血病容,皮肤及两侧巩膜有明显黄染,牙间隙明显增宽,脾在锁骨中线肋缘下4.5cm,质地较硬,肝仅能触及,下肢小 Patient, male, 19 years old. Due to the skin, eyes and yellow repeatedly anemia has been up to 9 years, on August 18, 1978 admission. Patients since childhood that face thin, often intermittent fever, accompanied by the skin, eyes repeatedly yellow and anemia, when light weight, had received liver drug treatment, because of ineffective to hospitalization. Physical examination: poor nutritional status, anemia, skin and sclera on both sides of the obvious yellow dye, significantly widening of the interphalangeal spleen in the midline of the clavicle under the costal 4.5cm, texture is hard, the liver can only touch the lower extremities