原发性心肌病也称特发性心肌病,它主要是指累及心肌的非血管性,非瓣膜性,原因未明的一类心肌病的统称。在心肌病中它是一种常见疾病。临床上主要表现心脏增大,心力衰竭,心律失常,心电异常及动脉栓塞等。在病理变化上有心脏体积增大,重量增加,心室扩张,心肌肥大及程度不等的纤维化,心肌变性坏死和炎症反应,附壁血栓形成也较常见。原发性心肌病在国外已有很多报 Primary cardiomyopathy, also known as idiopathic cardiomyopathy, which refers to the non-vascular involvement of non-cardiac, non-valvular, unexplained category of cardiomyopathy collectively. It is a common disease in cardiomyopathy. The main clinical manifestations of heart enlargement, heart failure, arrhythmia, ECG abnormalities and arterial embolism. Pathological changes in the heart volume increases, weight gain, ventricular dilatation, myocardial hypertrophy and varying degrees of fibrosis, myocardial necrosis and inflammatory reaction, mural thrombosis is also more common. Primary cardiomyopathy has been reported in many foreign countries