１３例原发性腹膜后脂肪肉瘤均经手术及病理证实。本病较少见，术前确诊较困难，但切除率较高（５３．８％），切除成功与否与就诊早晚、肿物大小及是否活动无明显关系。一经发现为腹膜后占位性病变．不应强求术前的定位及定性诊断，而应尽早剖腹探查，争取全部或部分切除肿瘤，必要时可将瘤体连同受侵脏器一并切除。对于复发病例争取再次以至多次手术切除。 13 cases of primary retroperitoneal liposarcoma were confirmed by surgery and pathology. This disease is less common. Preoperative diagnosis is more difficult, but the resection rate is higher (53.8%). Whether or not the resection is successful is not related to whether the treatment is sooner or later, the size of the tumor, and whether there is activity. Once discovered as retroperitoneal space-occupying lesions. Should not force preoperative positioning and qualitative diagnosis, but should be as soon as possible exploratory laparotomy, fighting for all or part of the removal of the tumor, if necessary, the tumor can be removed together with the affected organs. For recurrence cases to fight again and even more surgical resection.