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眼眶血管外皮瘤20例,其病理特点为:丰富的血管网,血管之间大量增生的梭形细胞,单个瘤细胞外有网状纤维包绕。根据肿瘤的异形程度及核分裂的数量诊断为良性、低度恶性及恶性血管外皮瘤,10岁以下患者诊断恶性要慎重。良性者局部切除应彻底,以防复发,恶性者应尽早行眼眶内容剜出术。放射治疗效果不肯定。本组病例平均随访6.3年,随访率14/20(70%).死亡率3/14(21.4%),健在者9例,存活最长者16年。
Orbital hemangiopericytoma in 20 cases, its pathological features: rich vascular network, a large number of blood vessels between the proliferation of spindle cells, a single tumor cells surrounded by reticular fibers. According to the degree of tumor and the number of mitotic diagnosis of benign, low grade malignant and malignant hemangiopericytoma, the diagnosis of malignancy in patients under 10 years should be cautious. Local excision of the benign should be thorough, in case of recurrence, malignant orbital content should be out of operation as soon as possible. Radiation therapy is not sure. The average follow-up of this group of patients was 6.3 years, the follow-up rate was 14/20 (70%). The mortality rate was 3/14 (21.4%), with 9 survivors and the highest survivors 16 years.