血管外皮瘤是一种比较少见的肿瘤,占全部血管性肿瘤的1%,通常见于下肢、腹膜后、躯干等处,发生于内脏组织及中枢神经系统者甚少,而发生于肝脏者更为罕见。现将我科遇到1例罕见的肝内恶性血管外皮瘤报告于下.患者,女性,7岁,以右上腹持续性疼痛伴发热3月之主诉入院.查体:患儿精神差,明显消瘦,全身浅表淋巴结不大,心、肺(-),右腹膨隆,肝上界右锁骨中线第4肋间,下界肋下7cm,剑突下4cm,质中,边缘钝,触疼(+),脾肋下未及;移动性浊音(-);CT 示肝脏巨大包 Hemangiopericytoma is a relatively rare tumor, accounting for 1% of all vascular tumors, usually found in the lower extremities, retroperitoneum, trunk, etc., occurs in the visceral tissue and central nervous system are very few, and in the liver more rare. Now we encounter a rare case of intrahepatic malignant hemangiopericytoma reported in the next patients, women, 7 years old, with persistent pain in the right upper quadrant with fever in March the main complaint admitted to the hospital. Thin, systemic superficial lymph nodes, heart, lung (-), right bulging, the upper right hepatic subclavian midline intercostal intercostal space 4, lower bounding ribs 7cm, xiphoid 4cm, quality, the edge of blunt, touch the pain +), Under the spleen and ribs; mobility dullness (-); CT showed a huge liver packet