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骨髓增生性疾病(myeloproliferativedisorder,MPD)系不明原因所致骨髓调节功能异常的一组综合征,本征包括一组恶性及潜在恶性的疾病,特点是骨髓各种成分不同程度增生,各种血细胞不同程度增多或减少,肝牌肿大(尤以脾肿大明显),出血倾向以及血栓形成。1951年 Dameshek 首先提出这一名称,以描述骨髓中三个造血系统的增生,包括慢性粒细胞白血病、真性红细胞增多症、巨核细胞白血病、Di Guglielmo 综台征(红血病、红白血病)、原发性脾髓样化生。尔后,他于1969年又提出将原发性出血性血小板增多症及造血早期细胞有发育紊乱的疾病如急性粒细胞白血病也包括在内。但由于细菌感染、急性出血、溶血反应等引起的一过性骨髓增生性反
Myeloproliferative disorder (MPD) is a group of syndromes characterized by unknown causes of bone marrow dysfunction. The syndrome includes a series of malignant and potentially malignant diseases characterized by various degrees of proliferation of various components of the bone marrow and various blood cells Increase or decrease the degree of liver enlargement (especially splenomegaly obvious), bleeding tendency and thrombosis. Dameshek first proposed this name in 1951 to describe the proliferation of three hematopoietic systems in the bone marrow including chronic myeloid leukemia, polycythemia vera, megakaryoblastic leukemia, Di Guglielmo syndrome (erythroleukemia, erythroleukemia) Pulmonary myeloid metaplasia. Later, he also proposed in 1969 the inclusion of primary hemorrhagic thrombocythemia and disorders in which hematopoietic cells have developmental disorders such as acute myeloid leukemia. However, due to bacterial infection, acute bleeding, hemolytic reaction caused by transient myelogenous anti-