近年来国外陆续有人报告一类特殊的淋巴网状系统疾病,称为伴巨大淋巴结肿的良性窦性组织细胞增生症(Sinus Histiocytosis with Massive Lymphadenopathy简称SHML)。此病的主要特征在于:大多数发病于儿童期,少数于青少年期;临床表现为无痛性淋巴结显著肿大(特别是颈部)、低热、白细胞增多和高γ球蛋白血 In recent years, one after another in foreign countries reported a class of diseases of the lymphatic system, known as with giant lymph nodes benign sinus hematosis (Sinus Histiocytosis with Massive Lymphadenopathy referred SHML). The main features of the disease are: most of the incidence in childhood, a few in adolescence; clinical manifestations of painless lymph nodes were significantly enlarged (especially the neck), fever, leukocytosis and high gamma globulin