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恶性淋巴瘤是一组高度异质性疾病 ,有关其分类研究过去一直是仁者见仁、智者见智 ,数种分类 (Rappaport,L ukes- Collins,WF及 Kiel等 )也各持所长、各抒己见 .近年证实 ,各型淋巴瘤均是独立的疾病实体 ,其准确定义除了依赖病理形态与免疫表型外 ,尚需考虑其遗传特性与临床表现 .在此基础上 ,“淋巴组织肿瘤欧美修改分类 (REAL )”与“淋巴造血组织肿瘤世界卫生组织分类 (WHO)”也应运而生 .作者就淋巴瘤分类研究的历史背景、REAL 与 WHO的特点及其发展趋势作一简要回顾和复习 .
Malignant lymphoma is a group of highly heterogeneous diseases. Its classification research has always been a beholder of the beholder and the wisdom of the wise. In the past few years, several categories (Rappaport, Lukes-Collins, WF, and Kiel, etc.) also held their own positions and expressed their opinions. It has been confirmed that all types of lymphomas are independent disease entities, and their precise definition requires the consideration of their genetic characteristics and clinical manifestations, in addition to their dependence on pathological morphology and immunophenotype. On this basis, “Lymphoid neoplasms are modified by European and American classifications (REAL). “)” and “The classification of lymphoid hematopoietic tissue World Health Organization (WHO)” came into being. The author made a brief review and review of the historical background of the classification of lymphoma, the characteristics of REAL and WHO and its development trend.