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SLE并发舞蹈病的报告极少,而以舞蹈病为最初体征的SLE更属罕见。本文报告一侧最初表现为舞蹈病的SLE。患者为一10岁女孩,因患舞蹈病5天入院。既往体健,入院前几个月无咽痛主诉,无神经系统疾病或胶原病家族史。体检见发育良好;两臂有明显的不随意运动;手指书写障碍,说话笨拙,发音困难;肌力正常,但肌张力增加,四肢运动不协调;其它物理和神经病学检查包括眼底均正常。实验室检验:WBC 3800,Hb 13.3g,血小板15万;血沉8 mm/h;肝功能试验、血清蛋白电泳、
SLE complicated with chorea is rarely reported, and chorea is the first sign of SLE is rare. This article reports on the SLE that initially showed chorea on one side. The patient was a 10-year-old girl who was hospitalized for 5 days with chorea. Past physical health, a few months before admission without sore throat complaints, no neurological disease or family history of collagen disease. Physical examination showed well-developed; arms were obviously involuntary movements; finger writing disorder, clumsiness in speech, difficulty in pronunciation; normal muscle strength but increased muscle tone and uncoordinated limb movements; other physical and neurological examinations included normal fundus. Laboratory tests: WBC 3800, Hb 13.3g, platelets 150,000; ESR 8 mm / h; liver function tests, serum protein electrophoresis,