恶性腱鞘巨细胞瘤临床上十分罕见，现将我院收治的1例报告如下。患者，男，39岁，1986年1月因左肘部肿块在当地职工医院行手术切除，病理检查为；“透明细胞瘤”。1987年3月左肘部再次出现肿块，逐渐长大，无疼痛，于1987年11月以“纤维肉瘤”收住我院。入院时见左肘后内侧肿块 Malignant giant cell tumor of tendon sheath is very rare in clinical practice. Now one case reported in our hospital is reported below. The patient, male, was 39 years old. In January 1986, a lump in his left elbow was surgically resected at a local staff hospital. His pathological examination was “clear cell tumor.” In March 1987, a lump appeared again in the left elbow, gradually grew up without pain, and she was admitted to our hospital with a “fibrosarcoma” in November 1987. Left cubital masses on admission