原发性小脑共济失调又称marie氏共济失调,是中枢神经系统变性病,病变主要累及小脑、脊髓侧索及下橄榄核,多有家族遗传史,本文对10例患者的临床与CT进行分析。一般资料本组男6例,女4例,年龄最大的52岁,最小18岁,有家族遗传史5例。10例均在入院时进行了CT检查。CT检查距发病时间1年内1例,1—2年4例,2—3年2例,3—4年2例,9年1例。 Primary cerebellar ataxia, also known as marie’s ataxia, is a degenerative disease of the central nervous system, the lesion mainly involves the cerebellum, spinal cord and the next olivary nucleus, and more family history of genetic, 10 cases of clinical and CT Analyze. General information The group of 6 males and 4 females, the oldest 52 years old, minimum 18 years old, 5 cases of family history. All 10 patients underwent CT examination on admission. CT examination from the time of onset within 1 year, 1 to 2 years in 4 cases, 2 to 3 years in 2 cases, 3 to 4 years in 2 cases, 9 years in 1 case.