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透明细胞肉瘤是一种罕见的高度恶性软组织肉瘤。多发于青少年及中年,以四肢远端的深部软组织多见,常与肌腱和腱膜相毗邻,易复发和转移。组织来源尚未明确,限制了有效的预后因素分析及治疗原则的确立。早期诊断和首次广泛切除是改善透明细胞肉瘤预后的关键。肿瘤大小与是否发生转移关系密切,是影响预后的重要因素。本文就透明细胞肉瘤的临床病理特点、鉴别诊断、临床治疗及预后分析的进展进行综述。
Clear cell sarcoma is a rare, highly malignant soft tissue sarcoma. Occur in adolescents and middle-aged, more often to the distal soft tissue of the limbs, often adjacent to the tendon and aponeurosis, recurrence and metastasis. The source of the organization is not yet clear, limiting the effective analysis of prognostic factors and the establishment of treatment principles. Early diagnosis and first extensive excision is the key to improving the prognosis of clear cell sarcoma. Tumor size and metastasis are closely related to prognosis is an important factor. This review summarizes the clinicopathological characteristics, differential diagnosis, clinical treatment and prognosis of clear cell sarcoma.