先天性横膈疝很少见,其发生率约为1/2,500次分娩,它是在受精后第10周,胎儿肠管从卵黄囊回到腹腔之前,由于胸腹膜形成不全引起的。在多数病例中,这种缺损是在横膈膜的后侧部分(foramen of bochdaleck),而且90%在左侧。横膈疝通常在出生后立即出现严重呼吸困难和肺萎陷,总的预后不佳。出生后生存率约为20%。偶尔这种情况在出生前因羊水过多可能疑诊,但多数情况偶然在产前诊断。超声诊断的标准包括心移位,有胃和/或肠管与心脏并排。腹部解剖异常,常常有一处显著的横膈缺损。右侧缺损诊断更困难,因为肝和肺的组织结构表现相似。本文报道一例罕见的右侧横膈疝,表现象胎儿 Congenital diaphragmatic hernia is rare with an incidence of about 1/2,500 births, which is caused by the formation of the thoracic-peritoneum before the fetal gut returns from the yolk sac to the peritoneal cavity 10 weeks after fertilization. In most cases, this defect is at the foramen of bochdaleck, with 90% on the left. Diaphragmatic hernia usually presents with severe dyspnea and lung collapse immediately after birth with poor overall prognosis. After birth, the survival rate is about 20%. Occasionally this situation may be suspected because of polyhydramnios before birth, but in most cases by chance in prenatal diagnosis. The criteria for ultrasound diagnosis include cardiac displacement, stomach and / or bowel alongside the heart. Abdominal anatomy is abnormal, there is often a significant diaphragmatic defect. Right-sided defect diagnosis is more difficult, because the liver and lung tissue structure similar. This article reports a rare right diaphragmatic hernia, the performance of the fetus