尿黑酸尿是一种罕见的常染色体隐性遗传病,系因体内尿黑酸氧化酶缺乏,使尿黑酸在体内堆积,经肾脏排泄后,使尿色异常。现将所见一例报道如下: 患儿女,1岁。因尿色异常于1984年11月27日入院。该患儿为抱养儿,抱养时尿色正常,但尿布经水浸泡后呈红色,用肥皂洗涤后立即变成棕黑色,有轻微特殊臭味。如尿液不经处理,放置后自行变色,两天后先变为深红色,逐渐变成棕黑色。 Urinary black acid is a rare autosomal recessive genetic disease, the Department of black urine acid in the body due to lack of acid oxidase, black urine acid accumulation in the body, excreted by the kidneys, so that abnormal urine color. Now see a case reported as follows: Children, 1 year old. Abnormal urine was admitted to hospital on November 27, 1984. The child was a toddler and had normal urine color when he was pregnant. However, the diaper was reddish after being soaked in water and turned brownish-black immediately after washing with soap, with a slight, special odor. Such as urine untreated, after placing their own color, two days later became dark red, gradually turned brown black.