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44例原发于眼附属器的非何杰金氏淋巴瘤,男32例,女12例,平均发病年龄45.7岁。有完整资料的36例中,眼睑及结膜19例,眼眶17例,其中3例儿童均原发于眼睑,在这35例中,根据临床表现分为急性型的8例(22.86%),慢性型28例(77.14%)。急性型起病急,迅速恶化,预后极差,组织病理学分型多属高度恶性淋巴瘤。慢性型起病及发展均较缓慢,预后较佳,组织病理学分型多属低发及中度恶性淋巴瘤。44例的组织病理学分型:结节型5例(11.36%),弥漫型39例(88.64%),属B细咆系的42例(95.45%),T细胞系2例(4.55%)。随访3年的26例,结节型的5例,无一例死亡:弥漫型的21例,死亡9例。
Forty-four non-Hodgkin’s lymphoma patients with primary appendage were 32 males and 12 females, with an average age of onset of 45.7 years. Of the 36 cases with complete information, there were 19 cases of eyelid and conjunctiva, 17 cases of orbital and 3 cases of children with primary eyelid. Among these 35 cases, 8 cases (22.86%) were classified into acute type according to clinical manifestations, Type 28 cases (77.14%). Acute acute onset, rapid deterioration, poor prognosis, mostly histopathological types of highly malignant lymphoma. Chronic onset and development are relatively slow, the prognosis is good, mostly histopathological classification of low-grade and moderately malignant lymphoma. The histopathological types of 44 cases were nodular type in 5 cases (11.36%) and diffuse type in 39 cases (88.64%). There were 42 cases (95.45%) in B cell line and 2 cases (4.55%) in T cell line. Twenty-six cases were followed up for 3 years and 5 cases were nodular. None died: diffuse 21 cases and 9 died.