报告无功能性原发性肾上腺皮质癌3例,术前确诊1例,误诊2例。因肿瘤侵犯较广未能切除者2例,分别于术后1～2月内死亡;完全切除1例,出院半月后复发并转移。文中对本病的发病率、临床表现、诊断、误诊、治疗及预后进行了讨论,认为本病恶性程度高,预后不良。 No functional primary adrenocortical carcinoma was reported in 3 cases. One case was diagnosed before surgery and 2 cases were misdiagnosed. 2 patients with unresectable tumors who died due to extensive tumor invasion died within 1 to 2 months postoperatively; 1 patient was completely resected and relapsed and metastasized after half a month of discharge. The morbidity, clinical manifestation, diagnosis, misdiagnosis, treatment and prognosis of the disease were discussed in this article. It is considered that the disease has high malignancy and poor prognosis.