本文报道 1例成人右室横纹肌瘤 ,肿瘤向心腔内突入阻塞右室流出道 ,临床貌似肺动脉瓣狭窄 ,由超声心动图诊断 ,手术病理证实。患者 ,女 ,37岁。主诉活动后心悸气短伴胸部憋闷进行性加重 4个月 ,经门诊 2ＤＥ检查发现右心占位性病变而入院。查体　双面颊略发绀 ,头颈、其他均未 This article reported one case of adult right ventricular rhabdomygioma, the tumor inwardly into the lumen blocking the right ventricular outflow tract, the clinical appearance of pulmonary valve stenosis, diagnosed by echocardiography, pathology confirmed. Patient, female, 37 years old. After the chief complaint activity, palpitations and shortness were accompanied by chest discomfort and aggravated for 4 months. After a 2DE examination on the outpatient clinic, right-heart occupying lesions were admitted to the hospital. Examination of the two sides of the cheeks slightly hair, head and neck, other are not