软组织肉瘤是间叶组织及与其交织生长的外胚层神经组织来源的恶性肿瘤,临床少见,占所有恶性肿瘤的1%以下[1]。2009年,美国新发软组织肉瘤病人为10 660例,死亡3820例。软组织肉瘤主要发生在四肢、躯干和腹膜后,腹膜后作为软组织肉瘤发病的重要部位之一,约占全身软组织肉瘤总数 Soft tissue sarcoma is a malignant tumor derived from mesenchymal tissue and its associated ectodermal nerve tissue, which is rare in clinical practice and accounts for less than 1% of all malignant tumors [1]. In 2009, there were 10 660 newly diagnosed soft tissue sarcomas in the United States and 3820 deaths. Soft tissue sarcoma occurs mainly in the limbs, trunk and retroperitoneal, retroperitoneal soft tissue sarcoma as an important part of the incidence, accounting for the total number of systemic soft tissue sarcoma