Wiskott-Aldrich 综合征(WAS),是一种少见的伴血小板减少和湿疹的联合免疫缺陷病。现报告1例。病历摘要男患,15个月。1986年4月23日因反复皮肤出血、湿疹、疖肿1年,鼻衄、柏油样便半个月入院。患儿自生后经常发热,患肺炎、中耳炎、面部湿疹久治不愈。6个月后,耳、腋下、颌下反复化脓感染,切开引流多次。近半个月出现柏油样便、口腔血泡、鼻衄、皮肤大片瘀斑。经输血、对症治疗,病情不见缓解而入院。患儿为足月顺产第1胎,父亲幼年患湿疹,祖母易患疖肿。查体:周身散在大小不等淤斑。面、颈、胸、背见边界尚滑的红斑、丘疹、鳞屑及色素沉着。左腋下2.0 Wiskott-Aldrich syndrome (WAS) is a rare combined immunodeficiency disorder with thrombocytopenia and eczema. Now report 1 case. Medical history male suffering, 15 months. April 23, 1986 due to repeated skin hemorrhage, eczema, boil for 1 year, epistaxis, asphaltene samples were admitted for half a month. Children often have fever after childbirth, suffering from pneumonia, otitis media, facial eczema persist for a long time. Six months later, the ears, armpit, subdural repeated pus infection, incision and drainage multiple times. Nearly two months asphalted stool, oral blood bubble, epistaxis, large skin ecchymosis. The blood transfusion, symptomatic treatment, the condition was relieved and admitted to hospital. Children with full-term first-born fetus, his father suffering from childhood eczema, grandmother prone to boil. Physical examination: whole body scattered in the size of ecchymosis. Face, neck, chest, back see the border is still smooth erythema, papules, scales and pigmentation. Left armpit 2.0