先天性完全性房室传导阻滞是一种少见病,但是对新生儿可构成潜在的生命威胁。据调查统计,该病在新生儿的发病率为1:20 000～1:22 000。令人感兴趣的是胶原性疾病与先天性完全性房室阻滞有联系。这种心脏传导系统的先天性损害是母体全身性疾病表现的一个方面,本例是母体红斑 Congenital complete atrioventricular block is a rare disease that can pose a potential life-threatening risk to newborns. According to the survey, the incidence of the disease in newborns was 1:20 000 ~ 1: 22 000. Interestingly, collagen disease is associated with congenital complete atrioventricular block. Congenital damage to this cardiac conduction system is one aspect of the manifestation of maternal systemic disease, in this case maternal erythema