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石骨症又名大理石骨病、广泛性脆性骨质硬化症、先天性骨硬化等,是一种病因未明的先天性骨发育障碍性疾病,主要特点是全身骨骼硬脆、骨密度增高、骨髓腔变窄甚至消失,临床表现为进行性贫血、肝脾肿大,容易骨折等。晚近由于石骨症引起骨髓病性贫血已非少见,现将我院收治的1例报告如下,并综合分析国内77例的血液学资料,着重讨论石骨症与骨髓病性贫血的关系。
Stone bone disease, also known as marble bone disease, extensive brittle sclerosis, congenital osteosclerosis, is an unknown etiology of congenital bone development disorders, the main features of systemic bones hard and brittle, increased bone mineral density, bone marrow Cavity narrowing or even disappear, the clinical manifestations of progressive anemia, hepatosplenomegaly, easy to fracture. Recently due to osteosarrosis caused by bone marrow anemia is not uncommon, now admitted to our hospital in 1 case report as follows, and a comprehensive analysis of 77 cases of hematology data, focusing on the relationship between osteosynthesis and myeloid anemia.