第一鳃裂发有异常较罕见，可分为二型，Ⅰ型多出现于成人期，表现为耳前、耳后及耳道内囊肿，深入外耳道，甚至终端达到中鼓室，源自外胚层，具有鳞状上皮树里，临床诊断较困难，可因囊肿压迫而致招风耳畸形和轻度传导性聋；1型多于儿童期即出现，可在较靠下方的下颌角下方出现 First gill anomalies are rare, can be divided into two types, type Ⅰ mostly in adulthood, the performance of the ear, ear and ear canal cysts, deep into the external auditory canal, and even reached the end of the tympanic cavity, derived from the ectoderm, With squamous epithelial tree, the clinical diagnosis is more difficult because of cyst compression can cause induced ear deformities and mild conductive deaf; type 1 appears more than in childhood, below the lower mandibular angle appears