郎格罕细胞组织细胞增生症(Langerhans cell histiocytosis,LCH)是一组病因不明、以病理性郎格罕细胞增生、浸润为主要特点的疾病,临床上成人LCH较少见,亦少累及上颌骨和腭部。本文报道了一例以腭部溃疡为主诉的成年LCH病例,并通过对近年相关文献的复习,介绍LCH的病因、临床损害特点、诊断标准、分类、治疗等。 Lange Langerhans cell histiocytosis (Langerhans cell histiocytosis, LCH) is a group of unknown etiology, pathological Langerhans cell proliferation, infiltration of the main features of the disease, clinical LCH is rare, and less involved in the maxilla And the palate. This article reports an example of patiENT ulcer-dominated adult LCH cases, and through the review of relevant literature in recent years, describes the etiology, clinical features, diagnostic criteria, classification, treatment of LCH.